DISPLAZIA FIBROASA
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DISPLAZIA FIBROASA
PREZENTARE DE CAZ
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Barbat 26 ani Dismorfism cranio- facial Scaderea brusca a acuitatii vizuale
AO Cefalee Fara antecedente patologice
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Displasia fibroasa Afectiune osoasa de etiologie
neprecizata Forma monostica si poliostica Simptome :deformitati faciale, ptoza
palpebrala,cefalee Deficite neurologice: scaderea
acuitatii vizuale, diminuarea auzului Tratament chirugical Scaderea acuitatii vizuale:chistul
displazic, hemoragia, mucocelul
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DISPLAZIA FIBROASA CU SCADEREA AVAUTOR V/S SCADEREA
AVLOCALIZARE CAUZE OBIECTIV
CHIRURGICALSEVEL,1984 9,f Acut,unilat Aripa sfenoid H n
Edgerton,1985
18,f Acut,unilat F,P,etmoid M n
15,f Cronic,unilat
Orbita,maxila C 6 rezectii
Derome,1986 21,f Acut,bilat Etaj anterior bil C hem n
13,f Acut,unilat F bilateral C n
5,m Chronic,bilat
Etaj anterior bil C n
osguthorpe1986
21.F Acut,unilat F, sfen, etm mixt biopsie
Kurokawa,1989
11,m
Acut,unilat Etmoid,sfenoid C hem n
Saito, 1990 4,f Cronic,unilat
F,etm,sfen simpla n
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DISPLAZIA FIBROASA CU SCADEREA AV
weisman1990
29,f Acut unil Maxilar, etm, sfn
M Rezectie plafon
Arroyo,1991 22,f Acut,unilat Aripa sfenoid,F simpla n
Bland, 1992 25,f Acut,unilat F,etmoid C craniotomie
Joseph, 1995 25,f Cronic,bilat Etm,sfn bilat C Decomp Co bil
Steel,1995 20,f Acut,unilat Sfn,etm M n
Chen,1997 28,m
Acut,unilat nespecificat evolutiv
Rezectie, CO
13,f Acut,unilat Sfn,etm C n
Katz,1998 32.m
Acut,unilat Plafon orbitar Chist anv
n
25,f Acut,unilat Etmoid,canal op
M re
19,f acut,unilat Baza craniu Chist anev
rezectie
16,f Acut,unilat Plafon orbitar b H n
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Concluzii Rezectia etajului anterior pentru
leziunile ce intereseaza orbita si sinusurile paranazale
Scaderea acuitatii vizuale este determinata de dezvoltarea unor leziuni compresive si nu de stenoza CO
Nu se recomanda decompresiunile profilactice
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PARTICULARITATE CAZ
Evacuarea leziunii chistice s-a facut la 6 saptamani de la debut iar pacientul a recapatat AV complet la OS si partial la OD
Pacientul dezvolta pareza nerv facial drept de tip periferic