Boala Kawasaky
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Transcript of Boala Kawasaky
BOALA KAWASAKY- Sindromul adenopatic-cutaneo-mucos- La copii , 10% vasculita de vase coronareHistologic PAN (proliferare intima, infiltrat cu mononucleare, anevrisme arteriale mici, tromboze)Tratament: Ig i.v. (400 mg/kg/zi), aspirinaPrognostic bun in majoritatea cazurilor Clinic: debut acut, febra, adenopatii nesupurate, conjunctivita,eritem pe mucoase, tegument (cavitate bucala, buze, limba) , descuamari periunghiale , miocardita, pericardita, aritmii, rar IMA. Paraclinic : sd. Inflamator , trombocitoza si crestere pasagera de transaminaze. Ekg unde Q patologice , tulburari de ritm si de conducere. Tratament : aspirina in doze mari ( 100 mg/ kg ) in faza acuta , Ig administrate i.v. Corticosteroizi sunt contraindicati.